HIRAYAMA DISEASE. CLINICAL CASE AND A REVIEW OF LITERATURE
E. R. Barantsevich,
D. I. Rudenko,
O. V. Posokhina,
A. A. Yakovlev, 
R. A. Gapeshin,
A. G. Smochilin,
E. O. Scherbakova
R. A. Gapeshin,
A. G. Smochilin,
E. O. Scherbakova https://doi.org/10.24884/1607-4181-2017-24-1-79-85
Abstract
Hirayama disease is a rare neurological disease with unilateral or asymmetric bilateral distal upper limb paresis and muscle atrophy. Here the authors report a clinical case of patient with weakness of cluster muscles and distal asymmetric upper paraparesis. Taking into consideration complaints, clinical presentation and performed follow-up examination (bloodwork, cervical MRI in neutral position and with flexion, MRI of lower limb muscles and electroneuromyography) the patient was diagnosed with Hirayama disease with asymmetric upper extremities. Also, there is a review of literature with pathogenesis, clinical presentation, diagnostic and treatment approaches to this disease.
About the Authors
E. R. Barantsevich
Federal State Budgetary Educational Institution of Higher Education «Academician I. P. Pavlov First St. Petersburg State Medical University» of the Ministry of Healthcare of the Russion Federation; Federal Almazov North-West Medical Research Centre
Russian Federation
Russian Federation
D. I. Rudenko
Federal State Budgetary Educational Institution of Higher Education «Academician I. P. Pavlov First St. Petersburg State Medical University» of the Ministry of Healthcare of the Russion Federation
Russian Federation
Russian Federation
O. V. Posokhina
Federal State Budgetary Educational Institution of Higher Education «Academician I. P. Pavlov First St. Petersburg State Medical University» of the Ministry of Healthcare of the Russion Federation
Russian Federation
Russian Federation
A. A. Yakovlev
Federal State Budgetary Educational Institution of Higher Education «Academician I. P. Pavlov First St. Petersburg State Medical University» of the Ministry of Healthcare of the Russion Federation
Russian Federation
Russian Federation
R. A. Gapeshin
Saint-Petersburg State University
Russian Federation
Russian Federation
Roman A. Gapeshin.
6-8 L’va Tolstogo street, Saint-Petersburg, 197022. Tel: +7(931) 223-40-93. E-mail: gapeshin.ra@gmail.com
A. G. Smochilin
Federal State Budgetary Educational Institution of Higher Education «Academician I. P. Pavlov First St. Petersburg State Medical University» of the Ministry of Healthcare of the Russion Federation; Saint-Petersburg State University
Russian Federation
Russian Federation
E. O. Scherbakova
Federal Almazov North-West Medical Research Centre
Russian Federation
Russian Federation
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Review
For citations:
Barantsevich E.R., Rudenko D.I., Posokhina O.V., Yakovlev A.A., Gapeshin R.A., Smochilin A.G., Scherbakova E.O. HIRAYAMA DISEASE. CLINICAL CASE AND A REVIEW OF LITERATURE. The Scientific Notes of the Pavlov University. 2017;24(1):79-85. (In Russ.) https://doi.org/10.24884/1607-4181-2017-24-1-79-85
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